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Perk Ablation Ameliorates Myelination in S63del-Charcot–Marie–Tooth 1B Neuropathy

In peripheral nerves, P0 glycoprotein accounts for more than 20% of myelin protein content. P0 is synthesized by Schwann cells, processed in the endoplasmic reticulum (ER) and enters the secretory pathway. However, the mutant P0 with S63 deleted (P0S63del) accumulates in the ER lumen and induces a d...

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Détails bibliographiques
Publié dans:ASN Neuro
Auteurs principaux: Musner, Nicolò, Sidoli, Mariapaola, Zambroni, Desireè, Del Carro, Ubaldo, Ungaro, Daniela, D’Antonio, Maurizio, Feltri, Maria L., Wrabetz, Lawrence
Format: Artigo
Langue:Inglês
Publié: SAGE Publications 2016
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4844932/
https://ncbi.nlm.nih.gov/pubmed/27095827
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1759091416642351
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