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Calcineurin Activity Is Increased in Charcot-Marie-Tooth 1B Demyelinating Neuropathy

Schwann cells produce a considerable amount of lipids and proteins to form myelin in the PNS. For this reason, the quality control of myelin proteins is crucial to ensure proper myelin synthesis. Deletion of serine 63 from P0 (P0S63del) protein in myelin forming Schwann cells causes Charcot-Marie-To...

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Detaylı Bibliyografya
Yayımlandı:J Neurosci
Asıl Yazarlar: Sidoli, Mariapaola, Reed, Chelsey B., Scapin, Cristina, Paez, Pablo, Cavener, Douglas R., Kaufman, Randal J., D'Antonio, Maurizio, Feltri, M. Laura, Wrabetz, Lawrence
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Society for Neuroscience 2021
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC8152608/
https://ncbi.nlm.nih.gov/pubmed/33879538
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.2384-20.2021
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