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Pathological ATX3 Expression Induces Cell Perturbations in E. coli as Revealed by Biochemical and Biophysical Investigations

Amyloid aggregation of human ataxin-3 (ATX3) is responsible for spinocerebellar ataxia type 3, which belongs to the class of polyglutamine neurodegenerative disorders. It is widely accepted that the formation of toxic oligomeric species is primarily involved in the onset of the disease. For this rea...

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Publicat a:Int J Mol Sci
Autors principals: Ami, Diletta, Sciandrone, Barbara, Mereghetti, Paolo, Falvo, Jacopo, Catelani, Tiziano, Visentin, Cristina, Tortora, Paolo, Ventura, Salvador, Natalello, Antonino, Regonesi, Maria Elena
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7835732/
https://ncbi.nlm.nih.gov/pubmed/33477953
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22020943
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