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Humanized mouse models of Cooley’s anemia: correct fetal-to-adult hemoglobin switching, disease onset, and disease pathology

β thalassemia major or Cooley’s Anemia (CA) has been difficult to model in mice due to their lack of a fetal hemoglobin gene equivalent. This summary describes novel preclinical humanized mouse models of CA that survive on human fetal hemoglobin at birth and are blood-transfusion dependent for life...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Ann N Y Acad Sci
Egile Nagusiak: Huo, Yongliang, McConnell, Sean C., Liu, Shanrun, Zhang, Tingting, Yang, Rui, Ren, Jinxiang, Ryan, Thomas M.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2010
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7791968/
https://ncbi.nlm.nih.gov/pubmed/20712771
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1749-6632.2010.05547.x
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