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Potential Contribution of Ryanodine Receptor 2 Upregulation to cGMP/PKG Signaling-induced Cone Degeneration in Cyclic Nucleotide-gated Channel Deficiency

Photoreceptor cyclic nucleotide-gated (CNG) channels regulate Ca(2+) influx in rod and cone photoreceptors. Mutations in cone CNG channel subunits CNGA3 and CNGB3 are associated with achromatopsia and cone dystrophies. Mice lacking functional cone CNG channel show endoplasmic reticulum (ER) stress-a...

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Detaylı Bibliyografya
Yayımlandı:FASEB J
Asıl Yazarlar: Yang, Fan, Ma, Hongwei, Butler, Michael R., Ding, Xi-Qin
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2020
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC7299158/
https://ncbi.nlm.nih.gov/pubmed/32173907
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1096/fj.201901951RR
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