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Cell-Autonomous Hedgehog Signaling Is Not Required for Cyst Formation in Autosomal Dominant Polycystic Kidney Disease

BACKGROUND: PKD1 or PKD2, the two main causal genes for autosomal dominant polycystic kidney disease (ADPKD), encode the multipass transmembrane proteins polycystin-1 (PC1) and polycystin-2 (PC2), respectively. Polycystins localize to the primary cilium, an organelle essential for cell signaling, in...

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Dades bibliogràfiques
Publicat a:J Am Soc Nephrol
Autors principals: Ma, Ming, Legué, Emilie, Tian, Xin, Somlo, Stefan, Liem, Karel F.
Format: Artigo
Idioma:Inglês
Publicat: American Society of Nephrology 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6830786/
https://ncbi.nlm.nih.gov/pubmed/31451534
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2018121274
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