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VCP maintains lysosomal homeostasis and TFEB activity in differentiated skeletal muscle

Differentiated tissue is particularly vulnerable to alterations in protein and organelle homeostasis. The essential protein VCP, mutated in hereditary inclusion body myopathy, amyotrophic lateral sclerosis and frontotemporal dementia, is critical for efficient clearance of misfolded proteins and dam...

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Detalhes bibliográficos
Publicado no:Autophagy
Main Authors: Arhzaouy, Khalid, Papadopoulos, Chrisovalantis, Schulze, Nina, Pittman, Sara K., Meyer, Hemmo, Weihl, Conrad C.
Formato: Artigo
Idioma:Inglês
Publicado em: Taylor & Francis 2019
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6526815/
https://ncbi.nlm.nih.gov/pubmed/30654731
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/15548627.2019.1569933
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