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Impaired IL-12- and IL-23-Mediated Immunity due to IL-12Rβ1 deficiency in Iranian Patients with Mendelian Susceptibility to Mycobacterial Disease

PURPOSE. Inborn errors of IFN-γ-mediated immunity underlie Mendelian Susceptibility to Mycobacterial Disease (MSMD), which is characterized by an increased susceptibility to severe and recurrent infections caused by weakly virulent mycobacteria, such as Bacillus Calmette–Guérin (BCG) vaccines and en...

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Dades bibliogràfiques
Publicat a:J Clin Immunol
Autors principals: Nekooie-Marnany, Nioosha, Deswarte, Caroline, Ostadi, Vajiheh, Bagherpour, Bahram, Taleby, Elaheh, Ganjalikhani Hakemi, Mazdak, Voyer, Tom Le, Rahimi, Hamid, Rosain, Jérémie, Pourmoghadas, Zahra, Sheikhbahaei, Saba, Khoshnevisan, Razieh, Petersheim, Daniel, Kotlarz, Daniel, Klein, Christoph, Boisson-Dupuis, Stéphanie, Casanova, Jean-Laurent, Bustamante, Jacinta, Sherkat, Roya
Format: Artigo
Idioma:Inglês
Publicat: 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6469360/
https://ncbi.nlm.nih.gov/pubmed/30255293
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10875-018-0548-1
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