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Impaired IL-12- and IL-23-Mediated Immunity due to IL-12Rβ1 deficiency in Iranian Patients with Mendelian Susceptibility to Mycobacterial Disease

PURPOSE. Inborn errors of IFN-γ-mediated immunity underlie Mendelian Susceptibility to Mycobacterial Disease (MSMD), which is characterized by an increased susceptibility to severe and recurrent infections caused by weakly virulent mycobacteria, such as Bacillus Calmette–Guérin (BCG) vaccines and en...

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Dettagli Bibliografici
Pubblicato in:J Clin Immunol
Autori principali: Nekooie-Marnany, Nioosha, Deswarte, Caroline, Ostadi, Vajiheh, Bagherpour, Bahram, Taleby, Elaheh, Ganjalikhani Hakemi, Mazdak, Voyer, Tom Le, Rahimi, Hamid, Rosain, Jérémie, Pourmoghadas, Zahra, Sheikhbahaei, Saba, Khoshnevisan, Razieh, Petersheim, Daniel, Kotlarz, Daniel, Klein, Christoph, Boisson-Dupuis, Stéphanie, Casanova, Jean-Laurent, Bustamante, Jacinta, Sherkat, Roya
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6469360/
https://ncbi.nlm.nih.gov/pubmed/30255293
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10875-018-0548-1
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