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Impaired IL-12- and IL-23-Mediated Immunity due to IL-12Rβ1 deficiency in Iranian Patients with Mendelian Susceptibility to Mycobacterial Disease

PURPOSE. Inborn errors of IFN-γ-mediated immunity underlie Mendelian Susceptibility to Mycobacterial Disease (MSMD), which is characterized by an increased susceptibility to severe and recurrent infections caused by weakly virulent mycobacteria, such as Bacillus Calmette–Guérin (BCG) vaccines and en...

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Detalhes bibliográficos
Publicado no:J Clin Immunol
Principais autores: Nekooie-Marnany, Nioosha, Deswarte, Caroline, Ostadi, Vajiheh, Bagherpour, Bahram, Taleby, Elaheh, Ganjalikhani Hakemi, Mazdak, Voyer, Tom Le, Rahimi, Hamid, Rosain, Jérémie, Pourmoghadas, Zahra, Sheikhbahaei, Saba, Khoshnevisan, Razieh, Petersheim, Daniel, Kotlarz, Daniel, Klein, Christoph, Boisson-Dupuis, Stéphanie, Casanova, Jean-Laurent, Bustamante, Jacinta, Sherkat, Roya
Formato: Artigo
Idioma:Inglês
Publicado em: 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6469360/
https://ncbi.nlm.nih.gov/pubmed/30255293
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10875-018-0548-1
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