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Bi-allelic c.181_183delTGT in BTB domain of KLHL7 is associated with overlapping phenotypes of Crisponi/CISS1-like and Bohring-Opitz like syndrome

Biallelic pathogenic variants in KLHL7 are known to result in Crisponi syndrome (CS)/cold-induced sweating syndrome type 1 (CISS1) like phenotype and Bohring-Opitz-like syndrome. In this report, a trio whole-exome sequencing (WES) was performed in proband with cold-induced sweating, microcephaly, fa...

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Bibliografski detalji
Izdano u:Eur J Med Genet
Glavni autori: Kanthi, Anil, Hebbar, Malavika, Bielas, Stephanie L, Girisha, Katta M, Shukla, Anju
Format: Artigo
Jezik:Inglês
Izdano: 2018
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Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6386622/
https://ncbi.nlm.nih.gov/pubmed/30142437
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ejmg.2018.08.009
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