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Mitochondrial alterations accompanied by oxidative stress conditions in skin fibroblasts of Huntington’s disease patients

Huntington disease (HD) is an autosomal dominant neurodegenerative disorder manifesting as progressive impairment of motor function and different neuropsychiatric symptoms caused by an expansion of CAG repeats in huntingtin gene (HTT). Mitochondrial dysfunction and bioenergetic defects can contribut...

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Publicado en:Metab Brain Dis
Autores principales: Jędrak, Paulina, Mozolewski, Paweł, Węgrzyn, Grzegorz, Więckowski, Mariusz R.
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer US 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6244791/
https://ncbi.nlm.nih.gov/pubmed/30120672
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11011-018-0308-1
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