Caricamento...

Mitochondrial alterations accompanied by oxidative stress conditions in skin fibroblasts of Huntington’s disease patients

Huntington disease (HD) is an autosomal dominant neurodegenerative disorder manifesting as progressive impairment of motor function and different neuropsychiatric symptoms caused by an expansion of CAG repeats in huntingtin gene (HTT). Mitochondrial dysfunction and bioenergetic defects can contribut...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Metab Brain Dis
Autori principali: Jędrak, Paulina, Mozolewski, Paweł, Węgrzyn, Grzegorz, Więckowski, Mariusz R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer US 2018
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6244791/
https://ncbi.nlm.nih.gov/pubmed/30120672
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11011-018-0308-1
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !