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Cardiac mTORC1 Dysregulation Impacts Stress Adaptation and Survival in Huntington’s Disease

Huntington’s disease (HD) is a dominantly inherited neurological disorder caused by CAG-repeat expansion in exon 1 of Huntingtin (HTT). But in addition to the neurological disease, mutant HTT (mHTT), which is ubiquitously expressed, impairs other organ systems. Indeed, epidemiological and animal mod...

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Detalles Bibliográficos
Publicado en:Cell Rep
Main Authors: Child, Daniel D., Lee, John H., Pascua, Christine J., Chen, Yong Hong, Monteys, Alejandro Mas, Davidson, Beverly L.
Formato: Artigo
Idioma:Inglês
Publicado: 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5967646/
https://ncbi.nlm.nih.gov/pubmed/29694882
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.celrep.2018.03.117
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