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Fine-Tuning ER Stress Signal Transducers to Treat Amyotrophic Lateral Sclerosis

Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease characterized by the progressive loss of motoneurons and paralysis. The mechanisms underlying neuronal degeneration in ALS are starting to be elucidated, highlighting disturbances in motoneuron proteostasis. Endoplasmic reticul...

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Detalles Bibliográficos
Publicado en:Front Mol Neurosci
Main Authors: Medinas, Danilo B., González, Jose V., Falcon, Paulina, Hetz, Claudio
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2017
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC5496948/
https://ncbi.nlm.nih.gov/pubmed/28725179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2017.00216
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