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Pulmonary fibrosis requires cell-autonomous mesenchymal fibroblast growth factor (FGF) signaling

Idiopathic pulmonary fibrosis (IPF) is characterized by progressive pulmonary scarring, decline in lung function, and often results in death within 3–5 five years after diagnosis. Fibroblast growth factor (FGF) signaling has been implicated in the pathogenesis of IPF; however, the mechanism through...

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Dettagli Bibliografici
Pubblicato in:J Biol Chem
Autori principali: Guzy, Robert D., Li, Ling, Smith, Craig, Dorry, Samuel J., Koo, Hyun Young, Chen, Lin, Ornitz, David M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Biochemistry and Molecular Biology 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5481550/
https://ncbi.nlm.nih.gov/pubmed/28487375
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M117.791764
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