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RyR(2)(R420Q) catecholaminergic polymorphic ventricular tachycardia mutation induces bradycardia by disturbing the coupled clock pacemaker mechanism

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a lethal genetic arrhythmia that manifests syncope or sudden death in children and young adults under stress conditions. CPVT patients often present bradycardia and sino-atrial node (SAN) dysfunction. However, the mechanism remains uncl...

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Dades bibliogràfiques
Publicat a:JCI Insight
Autors principals: Wang, Yue Yi, Mesirca, Pietro, Marqués-Sulé, Elena, Zahradnikova, Alexandra, Villejoubert, Olivier, D’Ocon, Pilar, Ruiz, Cristina, Domingo, Diana, Zorio, Esther, Mangoni, Matteo E., Benitah, Jean-Pierre, Gómez, Ana María
Format: Artigo
Idioma:Inglês
Publicat: American Society for Clinical Investigation 2017
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5396513/
https://ncbi.nlm.nih.gov/pubmed/28422759
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.91872
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