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Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation

Cystic fibrosis (CF), the most common lethal monogenic disease in Caucasians, is characterized by recurrent bacterial infections and colonization, mainly by Pseudomonas aeruginosa, resulting in unresolved airway inflammation. CF is caused by mutations in the gene coding for the cystic fibrosis trans...

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Bibliographic Details
Published in:Cell Death Dis
Main Authors: Ferrari, Eleonora, Monzani, Romina, Villella, Valeria R, Esposito, Speranza, Saluzzo, Francesca, Rossin, Federica, D'Eletto, Manuela, Tosco, Antonella, De Gregorio, Fabiola, Izzo, Valentina, Maiuri, Maria C, Kroemer, Guido, Raia, Valeria, Maiuri, Luigi
Format: Artigo
Language:Inglês
Published: Nature Publishing Group 2017
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Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC5386380/
https://ncbi.nlm.nih.gov/pubmed/28079883
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/cddis.2016.476
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