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Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation

Cystic fibrosis (CF), the most common lethal monogenic disease in Caucasians, is characterized by recurrent bacterial infections and colonization, mainly by Pseudomonas aeruginosa, resulting in unresolved airway inflammation. CF is caused by mutations in the gene coding for the cystic fibrosis trans...

Ausführliche Beschreibung

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Bibliographische Detailangaben
Veröffentlicht in:Cell Death Dis
Hauptverfasser: Ferrari, Eleonora, Monzani, Romina, Villella, Valeria R, Esposito, Speranza, Saluzzo, Francesca, Rossin, Federica, D'Eletto, Manuela, Tosco, Antonella, De Gregorio, Fabiola, Izzo, Valentina, Maiuri, Maria C, Kroemer, Guido, Raia, Valeria, Maiuri, Luigi
Format: Artigo
Sprache:Inglês
Veröffentlicht: Nature Publishing Group 2017
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5386380/
https://ncbi.nlm.nih.gov/pubmed/28079883
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/cddis.2016.476
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