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Proapoptotic protein Bim attenuates estrogen-enhanced survival in lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a progressive lung disease that primarily affects young women. Genetic evidence suggests that LAM cells bearing TSC2 mutations migrate to the lungs, proliferate, and cause cystic remodeling. The female predominance indicates that estrogen plays a critical role in LA...

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Detalhes bibliográficos
Publicado no:JCI Insight
Main Authors: Li, Chenggang, Li, Na, Liu, Xiaolei, Zhang, Erik Y., Sun, Yang, Masuda, Kouhei, Li, Jing, Sun, Julia, Morrison, Tasha, Li, Xiangke, Chen, Yuanguang, Wang, Jiang, Karim, Nagla A., Zhang, Yi, Blenis, John, Reginato, Mauricio J., Henske, Elizabeth P., Yu, Jane J.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Clinical Investigation 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5111508/
https://ncbi.nlm.nih.gov/pubmed/27882343
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.86629
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