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Transcriptional control of amino acid homeostasis is disrupted in Huntington’s disease

Disturbances in amino acid metabolism, which have been observed in Huntington’s disease (HD), may account for the profound inanition of HD patients. HD is triggered by an expansion of polyglutamine repeats in the protein huntingtin (Htt), impacting diverse cellular processes, ranging from transcript...

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Detalhes bibliográficos
Publicado no:Proc Natl Acad Sci U S A
Main Authors: Sbodio, Juan I., Snyder, Solomon H., Paul, Bindu D.
Formato: Artigo
Idioma:Inglês
Publicado em: National Academy of Sciences 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4978294/
https://ncbi.nlm.nih.gov/pubmed/27436896
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1608264113
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