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Cystathionine γ-lyase deficiency mediates neurodegeneration in Huntington’s disease

Huntington’s disease is an autosomal dominant disease associated with a mutation in the gene encoding huntingtin (Htt) leading to expanded polyglutamine repeats of mutant Htt (mHtt) that elicit oxidative stress, neurotoxicity, and motor and behavioural changes(1). Huntington’s disease is characteriz...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:Nature
Päätekijät: Paul, Bindu D., Sbodio, Juan I., Xu, Risheng, Vandiver, M. Scott, Cha, Jiyoung Y., Snowman, Adele M., Snyder, Solomon H.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2014
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC4349202/
https://ncbi.nlm.nih.gov/pubmed/24670645
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nature13136
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