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Recruitment of Light Chains by Homologous and Heterologous Fibrils Shows Distinctive Kinetic and Conformational Specificity

Light chain amyloidosis is a protein misfolding disease in which immunoglobulin light chains aggregate as insoluble fibrils that accumulate in extracellular deposits. Amyloid fibril formation in vitro has been described as a nucleation–polymerization, autocatalytic reaction in which nascent fibrils...

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Bibliografski detalji
Izdano u:Biochemistry
Glavni autori: Blancas-Mejía, Luis M., Ramirez-Alvarado, Marina
Format: Artigo
Jezik:Inglês
Izdano: 2016
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4968207/
https://ncbi.nlm.nih.gov/pubmed/27158939
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/acs.biochem.6b00090
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