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MACROPHAGE RECRUITMENT BY FIBROCYSTIN-DEFECTIVE BILIARY EPITHELIAL CELLS PROMOTES PORTAL FIBROSIS IN CONGENITAL HEPATIC FIBROSIS

Congenital Hepatic Fibrosis (CHF) is a disease of the biliary epithelium characterized by bile duct changes resembling ductal plate malformations and by progressive peribiliary fibrosis, in the absence of overt necroinflammation. Progressive liver fibrosis leads to portal hypertension and liver fail...

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Detalhes bibliográficos
Publicado no:Hepatology
Main Authors: Locatelli, Luigi, Cadamuro, Massimiliano, Spirli, Carlo, Fiorotto, Romina, Lecchi, Silvia, Morell, Carola Maria, Popov, Yury, Scirpo, Roberto, De Matteis, Maria, Amenduni, Mariangela, Pietrobattista, Andrea, Torre, Giuliano, Schuppan, Detlef, Fabris, Luca, Strazzabosco, Mario
Formato: Artigo
Idioma:Inglês
Publicado em: 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4764460/
https://ncbi.nlm.nih.gov/pubmed/26645994
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/hep.28382
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