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PKA dependent p-Ser-(675)β-catenin, a novel signaling defect in a mouse model of Congenital Hepatic Fibrosis
Genetically-determined loss of fibrocystin function causes Congenital Hepatic Fibrosis (CHF), Caroli Disease (CD) and Autosomal Recessive Polycystic Kidney Disease (ARPKD). Cystic dysplasia of the intrahepatic bile ducts and progressive portal fibrosis characterize liver pathology in CHF/CD. At a ce...
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Главные авторы: | , , , , , , , |
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Формат: | Artigo |
Язык: | Inglês |
Опубликовано: |
2013
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Предметы: | |
Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3800498/ https://ncbi.nlm.nih.gov/pubmed/23744610 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/hep.26554 |
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