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Prion-like propagation of mutant SOD1 misfolding and motor neuron disease spread along neuroanatomical pathways

A hallmark feature of amyotrophic lateral sclerosis (ALS) is that symptoms appear to spread along neuroanatomical pathways to engulf the motor nervous system, suggesting a propagative toxic entity could be involved in disease pathogenesis. Evidence for such a propagative entity emerged recently in s...

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Dades bibliogràfiques
Publicat a:Acta Neuropathol
Autors principals: Ayers, Jacob I., Fromholt, Susan E., O’Neal, Veronica M., Diamond, Jeffrey H., Borchelt, David R.
Format: Artigo
Idioma:Inglês
Publicat: 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4699876/
https://ncbi.nlm.nih.gov/pubmed/26650262
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-015-1514-0
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