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VPS54 and the wobbler mouse

The wobbler mouse is an animal model for human motor neuron disease, such as amyotrophic lateral sclerosis (ALS). The spontaneous, recessive wobbler mutation causes degeneration of upper and lower motor neurons leading to progressive muscle weakness with striking similarities to the ALS pathology. T...

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Detalles Bibliográficos
Publicado en:Front Neurosci
Autor Principal: Schmitt-John, Thomas
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2015
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4612502/
https://ncbi.nlm.nih.gov/pubmed/26539077
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnins.2015.00381
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