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Mutation in NRAS in familial Noonan syndrome – case report and review of the literature

BACKGROUND: Noonan syndrome (NS), a heterogeneous developmental disorder associated with variable clinical expression including short stature, congenital heart defect, unusual pectus deformity and typical facial features, is caused by activating mutations in genes involved in the RAS-MAPK signaling...

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Dettagli Bibliografici
Pubblicato in:BMC Med Genet
Autori principali: Ekvall, Sara, Wilbe, Maria, Dahlgren, Jovanna, Legius, Eric, van Haeringen, Arie, Westphal, Otto, Annerén, Göran, Bondeson, Marie-Louise
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4607013/
https://ncbi.nlm.nih.gov/pubmed/26467218
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12881-015-0239-1
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