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An ALS disease mutation in Cdc48/p97 impairs 20S proteasome binding and proteolytic communication

Cdc48 (also known as p97 or VCP) is an essential and highly abundant, double-ring AAA+ ATPase, which is ubiquitous in archaea and eukaryotes. In archaea, Cdc48 ring hexamers play a direct role in quality control by unfolding and translocating protein substrates into the degradation chamber of the 20...

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Publicat a:Protein Sci
Autors principals: Barthelme, Dominik, Jauregui, Ruben, Sauer, Robert T
Format: Artigo
Idioma:Inglês
Publicat: John Wiley & Sons, Ltd 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4570545/
https://ncbi.nlm.nih.gov/pubmed/26134898
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/pro.2740
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