Chargement en cours...

Spinal and bulbar muscular atrophy: pathogenesis and clinical management

Spinal and bulbar muscular atrophy, or Kennedy's disease, is an X-linked motor neuron disease caused by polyglutamine repeat expansion in the androgen receptor. The disease is characterised by weakness, atrophy and fasciculations in the limb and bulbar muscles. Affected males may have signs of...

Description complète

Enregistré dans:
Détails bibliographiques
Publié dans:Oral Dis
Auteurs principaux: Grunseich, C, Rinaldi, C, Fischbeck, KH
Format: Artigo
Langue:Inglês
Publié: 2013
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4284073/
https://ncbi.nlm.nih.gov/pubmed/23656576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/odi.12121
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!