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Spinal and bulbar muscular atrophy: pathogenesis and clinical management

Spinal and bulbar muscular atrophy, or Kennedy's disease, is an X-linked motor neuron disease caused by polyglutamine repeat expansion in the androgen receptor. The disease is characterised by weakness, atrophy and fasciculations in the limb and bulbar muscles. Affected males may have signs of...

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Detalhes bibliográficos
Publicado no:Oral Dis
Main Authors: Grunseich, C, Rinaldi, C, Fischbeck, KH
Formato: Artigo
Idioma:Inglês
Publicado em: 2013
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4284073/
https://ncbi.nlm.nih.gov/pubmed/23656576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/odi.12121
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