Cargando...

Spinal and bulbar muscular atrophy: pathogenesis and clinical management

Spinal and bulbar muscular atrophy, or Kennedy's disease, is an X-linked motor neuron disease caused by polyglutamine repeat expansion in the androgen receptor. The disease is characterised by weakness, atrophy and fasciculations in the limb and bulbar muscles. Affected males may have signs of...

Descrición completa

Gardado en:
Detalles Bibliográficos
Publicado en:Oral Dis
Main Authors: Grunseich, C, Rinaldi, C, Fischbeck, KH
Formato: Artigo
Idioma:Inglês
Publicado: 2013
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4284073/
https://ncbi.nlm.nih.gov/pubmed/23656576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/odi.12121
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!