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Spinal and bulbar muscular atrophy: pathogenesis and clinical management

Spinal and bulbar muscular atrophy, or Kennedy's disease, is an X-linked motor neuron disease caused by polyglutamine repeat expansion in the androgen receptor. The disease is characterised by weakness, atrophy and fasciculations in the limb and bulbar muscles. Affected males may have signs of...

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Bibliografiske detaljer
Udgivet i:Oral Dis
Main Authors: Grunseich, C, Rinaldi, C, Fischbeck, KH
Format: Artigo
Sprog:Inglês
Udgivet: 2013
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC4284073/
https://ncbi.nlm.nih.gov/pubmed/23656576
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/odi.12121
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