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Parkin-mediated ubiquitination of mutant glucocerebrosidase leads to competition with its substrates PARIS and ARTS

BACKGROUND: Parkinson’s disease (PD) is a movement neurodegenerative disorder characterized by death of dopaminergic neurons in the substantia nigra pars compacta of the brain that leads to movement impairments including bradykinesia, resting tremor, postural instability and rigidity. Mutations in s...

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Detalhes bibliográficos
Main Authors: Bendikov-Bar, Inna, Rapaport, Debora, Larisch, Sarit, Horowitz, Mia
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4074407/
https://ncbi.nlm.nih.gov/pubmed/24935484
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1750-1172-9-86
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