Lanean...

Loss of spastin function results in disease-specific axonal defects in human pluripotent stem cell-based models of hereditary spastic paraplegia

Human neuronal models of hereditary spastic paraplegias (HSP) that recapitulate disease-specific axonal pathology hold the key to understanding why certain axons degenerate in patients and to developing therapies. SPG4, the most common form of HSP, is caused by autosomal dominant mutations in the SP...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Denton, Kyle R., Lei, Ling, Grenier, Jeremy, Rodionov, Vladimir, Blackstone, Craig, Li, Xue-Jun
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2014
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3947148/
https://ncbi.nlm.nih.gov/pubmed/24123785
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/stem.1569
Etiketak: Etiketa erantsi
Etiketarik gabe, Izan zaitez lehena erregistro honi etiketa jartzen!