Cargando...

Loss of spastin function results in disease-specific axonal defects in human pluripotent stem cell-based models of hereditary spastic paraplegia

Human neuronal models of hereditary spastic paraplegias (HSP) that recapitulate disease-specific axonal pathology hold the key to understanding why certain axons degenerate in patients and to developing therapies. SPG4, the most common form of HSP, is caused by autosomal dominant mutations in the SP...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Denton, Kyle R., Lei, Ling, Grenier, Jeremy, Rodionov, Vladimir, Blackstone, Craig, Li, Xue-Jun
Formato: Artigo
Lenguaje:Inglês
Publicado: 2014
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3947148/
https://ncbi.nlm.nih.gov/pubmed/24123785
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/stem.1569
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!