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Prion Protein Misfolding, Strains, and Neurotoxicity: An Update from Studies on Mammalian Prions
Prion diseases, also known as transmissible spongiform encephalopathies (TSEs), are a group of fatal neurodegenerative disorders affecting humans and other mammalian species. The central event in TSE pathogenesis is the conformational conversion of the cellular prion protein, PrP(C), into the aggreg...
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| Autores principales: | , , |
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| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
Hindawi Publishing Corporation
2013
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3884631/ https://ncbi.nlm.nih.gov/pubmed/24454379 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2013/910314 |
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