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Does epithelial sodium channel hyperactivity contribute to cystic fibrosis lung disease?

Airway epithelia absorb Na(+) through the epithelial Na(+) channel (ENaC) and secrete Cl(−) through the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel. This balance maintains sufficient airway surface liquid hydration to permit efficient mucus clearance, which is needed to...

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Autori principali: Hobbs, Carey A, Da Tan, Chong, Tarran, Robert
Natura: Artigo
Lingua:Inglês
Pubblicazione: Blackwell Science Inc 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3784186/
https://ncbi.nlm.nih.gov/pubmed/23878362
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/jphysiol.2012.240861
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