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The Epithelial Sodium Channel (ENaC) as a Therapeutic Target for Cystic Fibrosis

Cystic fibrosis (CF) is a monogenic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. CFTR dysfunction is characterized by abnormal mucociliary transport due to a dehydrated airway surface liquid (ASL) and hyperviscous mucus, among other pathologies...

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Publicado en:Curr Opin Pharmacol
Main Authors: Shei, Ren-Jay, Peabody, Jacelyn E., Kaza, Niroop, Rowe, Steven M.
Formato: Artigo
Idioma:Inglês
Publicado: 2018
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6294660/
https://ncbi.nlm.nih.gov/pubmed/30340955
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.coph.2018.09.007
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