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Structural studies of cerebral cavernous malformations 2 (CCM2) reveal a folded helical domain at its C-terminus

Cerebral cavernous malformations (CCM) are neurovascular dysplasias affecting up to 0.5% of the population. Mutations in the CCM2 gene are associated with acquisition of CCM. We identify a previously uncharacterized domain at the C-terminus of CCM2 and determine its 1.9 Å resolution crystal structur...

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Autors principals: Fisher, Oriana S., Zhang, Rong, Li, Xiaofeng, Murphy, James W., Demeler, Borries, Boggon, Titus J.
Format: Artigo
Idioma:Inglês
Publicat: 2012
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3558538/
https://ncbi.nlm.nih.gov/pubmed/23266514
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.febslet.2012.12.011
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