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Tyrosine Residues Mediate Fibril Formation in a Dynamic Light Chain Dimer Interface

Light chain amyloidosis is an incurable protein misfolding disease where monoclonal immunoglobulin light chains misfold and deposit as amyloid fibrils, causing organ failure and death. Previously, we determined that amyloidogenic light chains AL-09 and AL-103 do not form fibrils at pH 10 (tyrosine p...

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Detalhes bibliográficos
Main Authors: DiCostanzo, Ara Celi, Thompson, James R., Peterson, Francis C., Volkman, Brian F., Ramirez-Alvarado, Marina
Formato: Artigo
Idioma:Inglês
Publicado em: American Society for Biochemistry and Molecular Biology 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3431636/
https://ncbi.nlm.nih.gov/pubmed/22740699
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M112.362921
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