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CTC1 Mutations in a Patient with Dyskeratosis Congenita

Dyskeratosis congenita (DC) is a rare inherited bone marrow failure syndrome caused by mutations in 7 genes involved in telomere biology, with approximately 50% of cases remaining genetically uncharacterized. We report a patient with classic DC carrying a compound heterozygous mutation in the CTC1 (...

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Autors principals: Keller, Rachel B., Gagne, Katelyn E., Usmani, G. Naheed, Asdourian, George K., Williams, David A., Hofmann, Inga, Agarwal, Suneet
Format: Artigo
Idioma:Inglês
Publicat: 2012
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3374040/
https://ncbi.nlm.nih.gov/pubmed/22532422
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/pbc.24193
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