Caricamento...

CTC1 Mutations in a Patient with Dyskeratosis Congenita

Dyskeratosis congenita (DC) is a rare inherited bone marrow failure syndrome caused by mutations in 7 genes involved in telomere biology, with approximately 50% of cases remaining genetically uncharacterized. We report a patient with classic DC carrying a compound heterozygous mutation in the CTC1 (...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Autori principali: Keller, Rachel B., Gagne, Katelyn E., Usmani, G. Naheed, Asdourian, George K., Williams, David A., Hofmann, Inga, Agarwal, Suneet
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2012
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3374040/
https://ncbi.nlm.nih.gov/pubmed/22532422
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/pbc.24193
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !