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Dyskeratosis congenita

Dyskeratosis congenita (DC) was originally defined as a rare inherited bone marrow failure syndrome associated with distinct mucocutaneous features. Today DC is defined by its pathogenetic mechanism and mutations in components of the telomere maintenance machinery resulting in excessively short telo...

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Autores principales: Bessler, Monica, Wilson, David B., Mason, Philip J.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2010
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3238451/
https://ncbi.nlm.nih.gov/pubmed/20493861
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.febslet.2010.05.019
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