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Defective lipid remodeling of GPI anchors in peroxisomal disorders, Zellweger syndrome, and rhizomelic chondrodysplasia punctata

Many cell surface proteins in mammalian cells are anchored to the plasma membrane via glycosylphosphatidylinositol (GPI). The predominant form of mammalian GPI contains 1-alkyl-2-acyl phosphatidylinositol (PI), which is generated by lipid remodeling from diacyl PI. The conversion of diacyl PI to 1-a...

Πλήρης περιγραφή

Αποθηκεύτηκε σε:
Λεπτομέρειες βιβλιογραφικής εγγραφής
Κύριοι συγγραφείς: Kanzawa, Noriyuki, Shimozawa, Nobuyuki, Wanders, Ronald J. A., Ikeda, Kazutaka, Murakami, Yoshiko, Waterham, Hans R., Mukai, Satoru, Fujita, Morihisa, Maeda, Yusuke, Taguchi, Ryo, Fujiki, Yukio, Kinoshita, Taroh
Μορφή: Artigo
Γλώσσα:Inglês
Έκδοση: The American Society for Biochemistry and Molecular Biology 2012
Θέματα:
Διαθέσιμο Online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3307642/
https://ncbi.nlm.nih.gov/pubmed/22253471
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M021204
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