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Endogenous surface expression of ΔF508 CFTR mediates cAMP-stimulated Cl(−) current in CFTR (ΔF508/ΔF508) pig thyroid epithelial cells

The Cystic Fibrosis Transmembrane Conductance Regulator, CFTR, is both an anion channel and a regulator of other transport proteins. CFTR gene mutations underlie the human disease, Cystic Fibrosis (CF). The most common CFTR mutation, ΔF508, produces a misfolded protein which traffics improperly. The...

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Autores principales: Li, Yonghai, Ganta, Suhasini, Fong, Peying
Formato: Artigo
Lenguaje:Inglês
Publicado: 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3253219/
https://ncbi.nlm.nih.gov/pubmed/21948195
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/expphysiol.2011.060756
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