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Amino acid substitution in NPC1 that abolishes cholesterol binding reproduces phenotype of complete NPC1 deficiency in mice

Substitution mutations in adjacent amino acids of the N-terminal domain of NPC1, a lysosomal membrane protein, abolish its cholesterol binding activity and impair its ability to export cholesterol from lysosomes of cultured cells lacking npc1 [Kwon HJ, et al. (2009) Cell 137:1213–1224]. Here, we sho...

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Bibliografische gegevens
Hoofdauteurs: Xie, Xuefen, Brown, Michael S., Shelton, John M., Richardson, James A., Goldstein, Joseph L., Liang, Guosheng
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: National Academy of Sciences 2011
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Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3174677/
https://ncbi.nlm.nih.gov/pubmed/21896731
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1112751108
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