A carregar...

Amino acid substitution in NPC1 that abolishes cholesterol binding reproduces phenotype of complete NPC1 deficiency in mice

Substitution mutations in adjacent amino acids of the N-terminal domain of NPC1, a lysosomal membrane protein, abolish its cholesterol binding activity and impair its ability to export cholesterol from lysosomes of cultured cells lacking npc1 [Kwon HJ, et al. (2009) Cell 137:1213–1224]. Here, we sho...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Main Authors: Xie, Xuefen, Brown, Michael S., Shelton, John M., Richardson, James A., Goldstein, Joseph L., Liang, Guosheng
Formato: Artigo
Idioma:Inglês
Publicado em: National Academy of Sciences 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3174677/
https://ncbi.nlm.nih.gov/pubmed/21896731
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1112751108
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!