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Chemical and/or Biological Therapeutic Strategies to Ameliorate Protein Misfolding Diseases

Inheriting a mutant misfolding-prone protein that cannot be efficiently folded in a given cell type(s) results in a spectrum of human loss-of-function misfolding diseases. The inability of the biological protein maturation pathways to adapt to a specific misfolding-prone protein also contributes to...

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Bibliografske podrobnosti
Main Authors: Ong, Derrick Sek Tong, Kelly, Jeffery W.
Format: Artigo
Jezik:Inglês
Izdano: 2010
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC3078197/
https://ncbi.nlm.nih.gov/pubmed/21146391
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ceb.2010.11.002
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