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Activation of the unfolded protein response is associated with impaired granulopoiesis in transgenic mice expressing mutant Elane

Severe congenital neutropenia (SCN) is an inborn disorder of granulopoiesis that in many cases is caused by mutations of the ELANE gene, which encodes neutrophil elastase (NE). Recent data suggest a model in which ELANE mutations result in NE protein misfolding, induction of endoplasmic reticulum (E...

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Autori principali: Nanua, Suparna, Murakami, Mark, Xia, Jun, Grenda, David S., Woloszynek, Jill, Strand, Marie, Link, Daniel C.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Hematology 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3072877/
https://ncbi.nlm.nih.gov/pubmed/21285438
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2010-10-311704
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