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Non-proteolytic functions of calpain-3 in sarcoplasmic reticulum in skeletal muscles

Mutations in CAPN3/Capn3, which codes for skeletal muscle-specific calpain-3/p94 protease, are responsible for limb-girdle muscular dystrophy type 2A (LGMD2A). Using “knock-in” (referred to as Capn3(CS/CS)) mice, in which the endogenous calpain-3 is replaced with a mutant calpain-3:C129S, that is pr...

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Autores principales: Ojima, Koichi, Ono, Yasuko, Ottenheijm, Coen, Hata, Shoji, Suzuki, Hidenori, Granzier, Henk, Sorimachi, Hiroyuki
Formato: Artigo
Lenguaje:Inglês
Publicado: 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3056149/
https://ncbi.nlm.nih.gov/pubmed/21295580
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jmb.2011.01.057
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