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Emergent Properties of Proteostasis in Managing Cystic Fibrosis

Cystic fibrosis (CF) is a consequence of defective recognition of the multimembrane spanning protein cystic fibrosis conductance transmembrane regulator (CFTR) by the protein homeostasis or proteostasis network (PN) ( Hutt and Balch (2010). Like many variant proteins triggering misfolding diseases,...

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Detalhes bibliográficos
Main Authors: Balch, William E., Roth, Daniela M., Hutt, Darren M.
Formato: Artigo
Idioma:Inglês
Publicado em: Cold Spring Harbor Laboratory Press 2011
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3039536/
https://ncbi.nlm.nih.gov/pubmed/21421917
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1101/cshperspect.a004499
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