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Emergent Properties of Proteostasis in Managing Cystic Fibrosis
Cystic fibrosis (CF) is a consequence of defective recognition of the multimembrane spanning protein cystic fibrosis conductance transmembrane regulator (CFTR) by the protein homeostasis or proteostasis network (PN) ( Hutt and Balch (2010). Like many variant proteins triggering misfolding diseases,...
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| Main Authors: | , , |
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| 格式: | Artigo |
| 語言: | Inglês |
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Cold Spring Harbor Laboratory Press
2011
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| 主題: | |
| 在線閱讀: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3039536/ https://ncbi.nlm.nih.gov/pubmed/21421917 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1101/cshperspect.a004499 |
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