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Prion Protein Misfolding Affects Calcium Homeostasis and Sensitizes Cells to Endoplasmic Reticulum Stress

Prion-related disorders (PrDs) are fatal neurodegenerative disorders characterized by progressive neuronal impairment as well as the accumulation of an abnormally folded and protease resistant form of the cellular prion protein, termed PrP(RES). Altered endoplasmic reticulum (ER) homeostasis is asso...

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Autors principals: Torres, Mauricio, Castillo, Karen, Armisén, Ricardo, Stutzin, Andrés, Soto, Claudio, Hetz, Claudio
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3012133/
https://ncbi.nlm.nih.gov/pubmed/21209925
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0015658
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