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Caspase-12 and endoplasmic reticulum stress mediate neurotoxicity of pathological prion protein

Prion diseases are characterized by accumulation of misfolded prion protein (PrP(Sc)), and neuronal death by apoptosis. Here we show that nanomolar concentrations of purified PrP(Sc) from mouse scrapie brain induce apoptosis of N2A neuroblastoma cells. PrP(Sc) toxicity was associated with an increas...

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Autori principali: Hetz, Claudio, Russelakis-Carneiro, Milene, Maundrell, Kinsey, Castilla, Joaquin, Soto, Claudio
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2003
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC213791/
https://ncbi.nlm.nih.gov/pubmed/14532116
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/emboj/cdg537
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